MAYER-ROKITANSKY-KUSTER-HAUSER SYNDROME (MRKH) PATIENT TREATED WITH LAPAROSCOPIC DAVYDOV PROCEDURE AT LIAQUAT NATIONAL HOSPITAL, KARACHI

Main Article Content

Dr Fatima Akram
Dr Aisha Taj
Dr Karam Un Nisa

Keywords

Mayer-Rokitansky-Kuster-Hauser Syndrome, Laparoscopic Davydov Procedure, Vaginal Reconstruction, Congenital Vaginal Agenesis, MRKH Syndrome Treatment

Abstract

Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome, characterized by congenital absence of the vagina and uterus, poses significant challenges to affected individuals, particularly in terms of fertility and sexuality. We present a case of a 20-year-old woman diagnosed with MRKH syndrome who underwent laparoscopic Davydov's vaginoplasty at Liaquat National Hospital, Karachi. The patient presented with primary amenorrhea and a blind-ended vagina, with normal external genitalia and well-developed secondary sexual characteristics. Surgical intervention was chosen after thorough counseling, and the Davydov procedure was performed successfully with minimal intraoperative complications. Postoperative care involved self-dilation with Hegar dilators, leading to satisfactory neovaginal length and function. Compared to traditional methods like the McIndoe procedure, the Davydov technique offers advantages such as fewer postoperative complications and a simpler surgical approach. Our case underscores the importance of individualized treatment strategies and multidisciplinary care in managing MRKH syndrome, with laparoscopic Davydov's vaginoplasty emerging as a promising option for vaginal reconstruction. Long-term follow-up is essential to assess the procedure's efficacy and patient satisfaction.

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